Myoclonic disorders

Subcategories

• 8A06.0 Essential myoclonus

  This is a hereditary form of myoclonus, which is not usually associated with epilepsy or any other medical condition. Essential myoclonus tends to be stable without increasing in severity over time. More recently, it is believed that essential myoclonus may be the same as myoclonus-dystonia caused by a mutation in the sarcoglycan gene. [1]

• 8A06.1 Segmental myoclonus

  Rhythmic or semi-rhythmic involuntary contractions of muscle groups supplied by one or more contiguous segments of the brainstem and/or spinal cord. [1]

• 8A06.2 Focal myoclonus

  Sudden, involuntary twitching or jerking of a muscle or group of muscles which effects a localised area of the body. [1]

Coded elsewhere

• Dystonia-plus (8A02.11)
• Facial myokymia (8B88.1)
• myoclonic epilepsy

References

1. World Health Organization. International Classification of Diseases, 11th Revision, for Mortality and Morbidity Statistics (ICD-11 MMS), 2026-01 release. World Health Organization; 2026.

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