Ataxic disorders

Description

Disorders associated with ataxia. The word "ataxia" comes from a Greek word meaning "lack of order, indiscipline". People with ataxia have problems with coordination because parts of the nervous system that control movement and balance are affected. Ataxia may affect the fingers, hands, arms, legs, body, speech, and eye movements. [1]

Subcategories

• 8A03.0 Congenital ataxia

  Congenital Ataxia is defined as a lack of coordination due to congenital abnormalities in the cerebellum. It is usually nonprogressive. [1]

• 8A03.1 Hereditary ataxia

  A group of genetic disorders characterised by slowly progressive incoordination of gait and often associated with poor coordination of hands, speech, and eye movements [1]

• 8A03.2 Non-hereditary degenerative ataxia

  Ataxia is characterized by incoordination, due to lesions in the cerebellum and efferent or afferent connections. Sporadic forms of ataxia that present without any family history or known genetic cause. Diagnosis is made after ruling out other causes of ataxia. [1]

• 8A03.3 Acquired ataxia

  Ataxia that is caused by a variety of exogenous and endogenous factors and is not clearly hereditary. May be seen in the setting of drug toxicity, post-viral cerebellitis, acute disseminated encephalomyelitis, traumatic brain injury, hypoxia, heat stroke, Wernicke’s encephalopathy, Miller Fisher syndrome, basilar migraine, or conversion reaction. [1]

References

1. World Health Organization. International Classification of Diseases, 11th Revision, for Mortality and Morbidity Statistics (ICD-11 MMS), 2026-01 release. World Health Organization; 2026.

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